Connective tissue disorders predispose to multiple compressions
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In our own patients (Sandmann/Scholbach) from 2005 to 12/3/2020, we observed the occurrence of combined vascular compression syndromes very frequently. Among them an unexpectedly high proportion of those with clinical evidence of connective tissue disease was found. A list of characteristic symptoms of genetic connective tissue diseases can be found here: Ehlers-Danlos syndrome, Marfan syndrome.

 

MALS — Median arcuate ligament syndrome/Plexus coeliacus — Kompressionssyndrom/Dunbar Syndrom

SMAS — Wilkie-Syndrom /Superior mesenteric artery syndrome

NCS— lordogenetic left renal vein compression aka Nutcracker syndrome

MTS— May Thurner syndrome

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